{"id":39801,"date":"2025-09-08T15:35:39","date_gmt":"2025-09-08T13:35:39","guid":{"rendered":"https:\/\/www.mylav.net\/?p=39801"},"modified":"2025-09-08T15:35:39","modified_gmt":"2025-09-08T13:35:39","slug":"quand-ce-nest-pas-un-lymphome-le-cas-rare-des-sarcomes-myeloides-chez-le-chien","status":"publish","type":"post","link":"https:\/\/www.mylav.net\/fr\/oncologie\/quand-ce-nest-pas-un-lymphome-le-cas-rare-des-sarcomes-myeloides-chez-le-chien\/","title":{"rendered":"Quand ce n\u2019est pas un lymphome\u2026 Le cas rare des sarcomes my\u00e9lo\u00efdes chez le chien"},"content":{"rendered":"<p>Un article r\u00e9cent a d\u00e9crit pour la premi\u00e8re fois trois cas de sarcome my\u00e9lo\u00efde chez le chien.<br \/>\nCette tumeur, issue de cellules my\u00e9lo\u00efdes, se d\u00e9veloppe dans les tissus solides, contrairement aux leuc\u00e9mies.<br \/>\nLe probl\u00e8me : sa pr\u00e9sentation clinique et cytologique est tr\u00e8s proche de celle d\u2019un lymphome canin. Mais son pronostic est malheureusement tr\u00e8s sombre \u00e0 court terme.<\/p>\n<p>D\u2019o\u00f9 l\u2019importance d\u2019un diagnostic rigoureux pour distinguer un lymphome (dont le pronostic et les options th\u00e9rapeutiques varient selon le sous-type) d\u2019un sarcome my\u00e9lo\u00efde.<\/p>\n<p><strong>Cas 1 &#8211; Un Dobermann avec une toux persistante<\/strong><\/p>\n<p><strong>Contexte clinique<\/strong><br \/>\nDobermann femelle st\u00e9rilis\u00e9e de 7 ans, pr\u00e9sent\u00e9e pour une toux \u00e9voluant depuis deux semaines.<\/p>\n<p><strong>R\u00e9sultats d\u2019analyses<\/strong><\/p>\n<ul>\n<li>H\u00e9mogramme et biochimie : normaux<\/li>\n<li>Radiographie thoracique : \u00e9panchement pleural + masse m\u00e9diastinale<\/li>\n<li>Cytologie du liquide pleural : cellularit\u00e9 mod\u00e9r\u00e9e (14,5 x10\u00b3 cellules\/\u03bcL), population pl\u00e9omorphe de cellules rondes avec petits lymphocytes, macrophages et cellules m\u00e9soth\u00e9liales r\u00e9actives<\/li>\n<li>Cytom\u00e9trie en flux : cellules CD11b+ (my\u00e9lo\u00efdes) et partiellement CD34+ (pr\u00e9curseurs h\u00e9matopo\u00ef\u00e9tiques) \u2192 diagnostic de n\u00e9oplasie my\u00e9lo\u00efde, exclusion d\u2019un lymphome<\/li>\n<\/ul>\n<p><strong>\u00c9volution<\/strong><br \/>\nUne semaine plus tard : infiltration sanguine massive par cellules indiff\u00e9renci\u00e9es, avec an\u00e9mie et thrombop\u00e9nie (\u00e9volution vers une leuc\u00e9mie my\u00e9lo\u00efde aigu\u00eb).<br \/>\nAucun traitement instaur\u00e9.<br \/>\nD\u00e9c\u00e8s apr\u00e8s 20 jours.<br \/>\nL\u2019autopsie a confirm\u00e9 une infiltration multi-organes.<\/p>\n<p><strong>Cas 2 &#8211; Une Golden Retriever avec ad\u00e9nom\u00e9galie g\u00e9n\u00e9ralis\u00e9e<\/strong><\/p>\n<p><strong>Contexte clinique<\/strong><br \/>\nGolden Retriever femelle de 6 ans, pr\u00e9sentant une ad\u00e9nom\u00e9galie g\u00e9n\u00e9ralis\u00e9e et une hypertrophie amygdalienne.<\/p>\n<p><strong>R\u00e9sultats d\u2019analyses<\/strong><\/p>\n<ul>\n<li>H\u00e9mogramme : normal<\/li>\n<li>Cytologie des noeuds : grandes cellules rondes + pr\u00e9curseurs my\u00e9lo\u00efdes \u00e0 diff\u00e9rents stades de maturation<\/li>\n<li>Cytom\u00e9trie en flux : cellules CD11b+ et partiellement CD34+ \u2192 diagnostic de tumeur my\u00e9lo\u00efde, lymphome \u00e9cart\u00e9 malgr\u00e9 un profil oligoclonal en PARR<\/li>\n<li>Sang et moelle : pas d\u2019infiltration initiale<\/li>\n<\/ul>\n<p><strong>\u00c9volution<\/strong><br \/>\nSurveillance par h\u00e9mogrammes successifs \u2192 apparition de cytop\u00e9nies progressives et de cellules indiff\u00e9renci\u00e9es.<br \/>\nMise en place d\u2019une chimioth\u00e9rapie \u00e0 base de cytarabine.<br \/>\nD\u00e9c\u00e8s apr\u00e8s 3 mois.<\/p>\n<p><strong>Cas 3 &#8211; Un crois\u00e9 en traitement cortico\u00efde pour suspicion de lymphome<\/strong><\/p>\n<p><strong>Contexte clinique<\/strong><br \/>\nCrois\u00e9 m\u00e2le castr\u00e9 de 11 ans, trait\u00e9 par cortico\u00efdes depuis un mois pour suspicion clinique et cytologique de lymphome, avec ad\u00e9nom\u00e9galie g\u00e9n\u00e9ralis\u00e9e.<\/p>\n<p><strong>R\u00e9sultats d\u2019analyses<\/strong><\/p>\n<ul>\n<li>H\u00e9mogramme : normal<\/li>\n<li>Cytologie des noeuds : grandes cellules rondes pr\u00e9dominantes<\/li>\n<li>Cytom\u00e9trie en flux : cellules CD11b+ et partiellement CD14+ (monocytes)<\/li>\n<li>Sang et moelle : n\u00e9gatifs pour infiltration<\/li>\n<\/ul>\n<p><strong>\u00c9volution<\/strong><br \/>\nPoursuite du traitement cortico\u00efde d\u00e9j\u00e0 instaur\u00e9.<br \/>\nD\u00e9c\u00e8s un mois plus tard.<\/p>\n<p><strong>Commentaire<\/strong><\/p>\n<p>Ces trois cas avaient en commun une pr\u00e9sentation clinique et cytologique trompeuse, mimant un lymphome canin (ad\u00e9nom\u00e9galie g\u00e9n\u00e9ralis\u00e9e, masse m\u00e9diastinale). Dans le second cas, la pr\u00e9sence de pr\u00e9curseurs my\u00e9lo\u00efdes \u00e0 diff\u00e9rents stades avait m\u00eame fait suspecter une my\u00e9lopo\u00ef\u00e8se extram\u00e9dullaire.<\/p>\n<p>Le sarcome my\u00e9lo\u00efde est une n\u00e9oplasie h\u00e9matopo\u00ef\u00e9tique rare, issue des pr\u00e9curseurs my\u00e9lo\u00efdes. Il peut \u00eatre consid\u00e9r\u00e9 comme une forme extram\u00e9dullaire atypique de leuc\u00e9mie my\u00e9lo\u00efde aigu\u00eb (LMA). Contrairement \u00e0 la LMA classique, il se manifeste d\u2019abord par des masses solides et n\u2019atteint le sang et la moelle que secondairement.<\/p>\n<p><strong>Pourquoi cela concerne la pratique clinique ?<\/strong><\/p>\n<ul>\n<li>Ces tumeurs, bien que rares, doivent figurer dans la liste des diagnostics diff\u00e9rentiels lors d\u2019une suspicion de lymphome.<\/li>\n<li>Apr\u00e8s la cytologie, l\u2019analyse de choix est la cytom\u00e9trie en flux : elle permet d\u2019identifier la lign\u00e9e cellulaire (lympho\u00efde vs my\u00e9lo\u00efde), ce que la cytologie seule ne permet pas.<\/li>\n<li>La PARR peut confirmer la nature tumorale mais pas la lign\u00e9e, comme illustr\u00e9 dans le cas 2.<\/li>\n<li>Le pronostic reste d\u00e9favorable : \u00e0 ce jour, aucun traitement r\u00e9ellement efficace n\u2019est d\u00e9crit, comme pour la majorit\u00e9 des LMA.<\/li>\n<\/ul>\n<p>\u00c0 noter : le seul chien ayant surv\u00e9cu le plus longtemps (3 mois) \u00e9tait aussi le seul \u00e0 avoir re\u00e7u une chimioth\u00e9rapie.<\/p>\n<p><strong>R\u00e9f\u00e9rence<\/strong><\/p>\n<p>Ubiali A, Martini V, Comazzi S, Iussich S, Miniscalco B, Poggi A, Morello E, Roccabianca P, R\u00fctgen B, Zamboni C, Riondato F.<br \/>\n<em>Granulocytic neoplasm suggestive of primary myeloid sarcoma in 3 dogs.<\/em><br \/>\nVeterinary Pathology 2025;62(1):48-52<\/p>\n<p><strong>Valeria Martini<\/strong>, DMV, PhD &#8211; Experte MYLAV en Cytom\u00e9trie en flux<br \/>\n<strong>Walter Bertazzolo<\/strong>, DMV, EBVS European Specialist in Veterinary Clinical Pathology (Dipl. ECVCP), Directeur scientifique de MYLAV<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Un article r\u00e9cent a d\u00e9crit pour la premi\u00e8re fois trois cas de sarcome my\u00e9lo\u00efde chez [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":39802,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"inline_featured_image":false,"footnotes":""},"categories":[1124],"tags":[],"class_list":["post-39801","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-oncologie"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.3 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Quand ce n\u2019est pas un lymphome\u2026 Le cas rare des sarcomes my\u00e9lo\u00efdes chez le chien - MyLav<\/title>\n<meta name=\"description\" content=\"Un article r\u00e9cent a d\u00e9crit pour la premi\u00e8re fois trois cas de sarcome my\u00e9lo\u00efde chez le chien.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.mylav.net\/fr\/oncologie\/quand-ce-nest-pas-un-lymphome-le-cas-rare-des-sarcomes-myeloides-chez-le-chien\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Quand ce n\u2019est pas un lymphome\u2026 Le cas rare des sarcomes my\u00e9lo\u00efdes chez le chien - 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